KMID : 1038120170500040400
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Clinical Endoscopy 2017 Volume.50 No. 4 p.400 ~ p.403
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Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones
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Hwang Moon-Joo
Kim Tae-Nyeun
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Abstract
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Caroli disease (CD) is a rare congenital malformation of the liver characterized by non-obstructive, segmental, cystic dilatation of the intrahepatic bile ducts (IHDs). The clinical course is usually asymptomatic for the first 5?20 years, and symptoms may seldom occur throughout the patient¡¯s life. Bile stagnation leads to recurrent episodes of cholangitis, stone formation, or liver abscesses, and biliary cirrhosis usually occurs years later. Here we report on a 42-year-old man diagnosed with diffuse-type CD with a characteristic central dot sign, who had multiple intrahepatic and common bile duct (CBD) stones. CBD stones were treated successfully with endoscopic retrograde cholangiopancreatography (ERCP).
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KEYWORD
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Caroli disease, Choledocholithiasis, Central dot sign, Endoscopic retrograde cholangiopancreatography
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